This term is used to refer to a heterogeneous group of retinal disorders that lead to progressive loss of visual acuity, visual field defects, and night blindness. The name retinitis pigmentosa comes from the pigment deposits that characterize these disorders. In their classic form (see findings and diagnostic considerations) of such disorders, these deposits progress from the periphery to the center of the retina.
Epidemiology: The worldwide incidence of retinitis pigmentosa is estimated at between one per 35000 and one per 70000 persons. The estimated incidence of mutated alleles is one per 80 persons.
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