Coats Disease Definition

Congenital retinal telangiectasia with vascular anomalies that nearly always presents unilaterally and can lead to exudation and eventually to exudative retinal detachment.

Epidemiology: This rare disorder manifests itself in young children and teenagers. Boys are usually affected (in about 90% of all cases).

H Coats' disease usually occurs in young and teenage boys. It is nearly always unilateral.

Pathogenesis: Telangiectasia and aneurysms lead to exudation and eventually to retinal detachment.

Symptoms: The early stages are characterized by loss of visual acuity, the later stages by leukocoria (white pupil; see Fig. 12.36) or unilateral strabismus, although the combination of leukocoria and strabismus is also possible.

Diagnostic considerations and findings: Ophthalmoscopy will reveal telan-giectasia, subretinal whitish exudate with exudative retinal detachment and hemorrhages (Fig. 12.21).

Differential diagnosis: In the advanced stages of the disorder, retinoblas-toma should be excluded by ophthalmoscopy and retinopathy of prematurity on the basis of the patient's history. Both disorders may also cause leukocoria.

Treatment: The treatment of choice is laser photocoagulation or cryotherapy to destroy anomalous vasculature.

Coats Disease Retina Changes

Fig. 12.21 Typical vascular changes of telangiectasia (arrow) accompanied by exudative retinal detachment with numerous lipid deposits (arrowheads).

Fig. 12.21 Typical vascular changes of telangiectasia (arrow) accompanied by exudative retinal detachment with numerous lipid deposits (arrowheads).

Prognosis: Left untreated, the disease will eventually cause blindness due to total retinal detachment. Treatment is effective in preventing blindness in about 50% of all patients.

How To Deal With Rosacea and Eczema

How To Deal With Rosacea and Eczema

Rosacea and Eczema are two skin conditions that are fairly commonly found throughout the world. Each of them is characterized by different features, and can be both discomfiting as well as result in undesirable appearance features. In a nutshell, theyre problems that many would want to deal with.

Get My Free Ebook


Post a comment