The retinal cavernous hemangioma typically appears as a globular or sessile intraretinal lesion that is composed of multiple vascular channels that have a reddish-blue color . It may show patches of gray-white fibrous tissue on the surface, but it does not cause the exudation that characterizes the retinal capillary hemangioma. Cavernous hemangioma is a congenital retinal vascular hamartoma that is probably present at birth. This tumor can be associated with similar intracranial and cutaneous vascular hamartomas, but the syndrome does not have the visceral tumors that characterize the von Hippel Lindau syndrome. As a general rule, retinal cavernous hemangioma requires no active treatment. If vitreous hemorrhage should occur, laser or cryotherapy to the tumor can be attempted. If vitreous blood does not resolve, removal by vitrectomy may be necessary.
Fig. 8.15. Retinal astrocytic hamartoma with glistening calcification lesion or it can be part of the Wyburn Mason syndrome, which is characterized by other similar lesions in the midbrain and sometimes the orbit, mandible, and maxilla. It does not appear to have a hereditary tendency.
Was this article helpful?