Retinal capillary hemangioma is a reddish pink retinal mass that can occur in the peripheral fundus or adjacent to the optic disc . The tumor often has prominent dilated retinal blood vessels that supply and drain the lesion (Fig. 8.13). Untreated lesions can cause intraretinal exudation and retinal detachment. Fluorescein angiography shows rapid filling of the tumor with dye and intense late staining of the mass. Patients with retinal capillary hemangioma should be evaluated for the von Hippel Lindau syndrome, an autosomal dominant condition characterized by cerebellar hemangioblastoma, pheochromocytoma, hypernephroma, and other visceral tumors and cysts. If the tumor produces macular exudation
of retinal detachment, it can be treated with methods of laser photocoagulation, cryotherapy, photodynamic therapy, plaque radiotherapy, or external beam radiotherapy. The gene responsible or this syndrome has been localized to the short arm of chromosome 3.
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