Lymphangioma is a common vascular tumor in children. This tumor comprised 0.3 to 1.5% of all orbital biopsies in five orbital tumor series (Table 14.1).1-5 The real frequency may be higher because some asymptomatic and mildly symptomatic cases do not undergo biopsy. Lymphangioma most commonly presents in patients under 10 years of age. However, it is sometimes detected later in life following trauma and intralesional hemorrhage. In such cases, the diagnosis is difficult. In contrast to capillary hemangioma, lymphangiomas do not regress spontaneously. However, they generally become more encapsulated in later years of life as a result of the tendency of the body to form a barrier to further tumor expansion.
When studied with arteriography or venography, lymphangiomas show no demonstrable connections to the venous system.6 This is in contrast to orbital varices, which usually demonstrate connections to the venous system.
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