Prognosis

Most patients with SM have only slowly progressive disease and many survive several decades. 33% evolve into a haematological malignancy, frequently leukaemia. Mast cell leukaemia is resistant to intensive chemotherapy and has a survival of only a few months.

Escribano, L. et al. (2002) Mastocytosis: current concepts in diagnosis and treatment. Ann Hematol, 81, 677-690; Valent, P. et al. (2001) Diagnostic criteria and classification of mastocytosis: a consensus proposal. Leuk Res, 25, 603-625.

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